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A rare case report of malignant peripheral nerve sheath tumor involving both the small bowel and large bowel
Nazia Khan1, Irma Hashmi2, Liana Atallah2, Hamid Shaaban3, Gunwant Guron3, Andre Fedida1
1 Department of Gastroenterology, St. Michael's Medical Center, Newark, NJ, an Affiliate of New York Medical College, Westchester, NY, USA
2 Department of Internal Medicine, St. Michael's Medical Center, Newark, NJ, an Affiliate of New York Medical College, Westchester, NY, USA
3 Department of Medical Oncology, St. Michael's Medical Center, Newark, NJ, an Affiliate of New York Medical College, Westchester, NY, USA
Correspondence Address:
Dr. Hamid Shaaban
111 Central Avenue, Newark, NJ 07102
USA
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/aam.aam_10_20
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Malignant peripheral nerve sheath tumor (MPNST) contains properties and histologic markers of both neural crest cells and mesenchymal cells. It is a rare diagnosis, with an incidence of 1:100,000/year or 4%–10% of soft-tissue sarcomas. There are very few cases reported and studied. Therefore, establishing a proper diagnosis and treatment of MPNST provides a challenge. We present this unique and rare case of metastatic MPNST of the small and large bowel with bone, pulmonary, liver, and splenic metastases. The patient subsequently developed hemorrhagic brain metastases and died 6 months after THE initial diagnosis.
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